Medical Xpress: Hemic and Lymphatic Diseases: News and Research on Sezary Syndrome Sezary syndrome | About the Disease | GARD - Genetic and Rare Diseases ... Although the condition can affect people of all ages, it is commonly diagnosed in adults over age 60. [7][3] The dominant signs and symptoms of the disease are: Sézary syndrome in a 61-year-old man presenting in 1972 with unrelenting itchiness of six months' duration.
People with Sezary syndrome are more likely to get infections because the skin barrier is damaged and the immune system is weakened. These infections can be serious and may include bacterial, viral or fungal infections. Sezary syndrome is an aggressive form of cutaneous T-cell lymphoma which is a group of disorders that occur when T-cells (a type of white blood cell) become cancerous and affect the skin. Sézary syndrome (SS) is an aggressive cutaneous T cell lymphoma (CTCL) that presents with skin disease (usually erythroderma) plus a high burden of circulating malignant T lymphocytes ("Sézary cells").
sezary's disease, Patients may also have lymph node and/or visceral organ involvement. Doctors don’t know the exact cause of this disease, but a small number of people with Sézary syndrome have human T-lymphotropic viruses type 1 and type 2. This virus is passed from one person to... Sézary Syndrome is an ultra-rare, debilitating form of lymphoma affecting an estimated 1 in 10,000,000 people worldwide, though available estimates vary wildly. The goal is to help eliminate this disease over time using medical science and patient support as the North Stars.
